Choledochal cyst. An extremely rare malformation with potential severe complications

Autori

  • Enrica Antonelli Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina
  • Pietro Impellizzeri Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina
  • Salvatore Arena Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina
  • Saveria Parisi Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina
  • Flora Maria Peri Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina
  • Rosario Caruso Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina
  • Jean De Ville de Goyet ISMETT, Palermo
  • Carmelo Romeo Department of Human Pathology of Adult and Childhood “G.Barresi”, Unit of Pediatric Surgery, University of Messina, Messina

DOI:

https://doi.org/10.6092/1828-6550/APMB.106.2.2018.A6

Parole chiave:

Choledocal cyst, hepaticojejunostomy, malformation jaundice

Abstract

Introduction: Choledocal cysts (CC) are rare congenital dilations of the extrahepatic and/or intrahepatic biliary tree with heterogeneous clinical pictures and high risk of malignancy. Case report: We reported a clinical case of 9 years old child with abdominal pain and jaundice. Strumental investigation with ultrasonography and magnetic resonance showed a CC. For this reason the patient underwent CC surgical excision and hepaticojejunostomy. Conclusion: CCs are a rare desease entity in Caucasian, with potential severe complications. Anearly diagnosis and a long.term follow-up is recommended

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Pubblicato

2018-12-18

Fascicolo

Sezione

CLINICAL CASE SEMINAR